EARLY ORAL REHABILITATION OF A CHILD WITH AMELOGENESIS IMPERFECTA: A CASE REPORT By Dr.Deepa Vinod Bhat, IInd year P.G.T., Dep. of Pediatric Dentistry, R.A.D.C & H, Kolkata-14. Abstract Managing a menace.....A faded hope revived to an unending happiness. The term amelogenesis imperfecta has been defined to include a variety of genetically determined disorders that primarily affect the enamel of all or nearly all the teeth without causing detectable alteration elsewhere in the body. Thus amelogenesis imperfect represents an inherited group of anomalies of enamel formation with an incidence of 1:718 to 1:14,000. AI follows an autosomal dominant, autosomal recessive or x-linked pattern of inheritance. The main clinical characteristics are extensive loss of tooth tissue, poor esthetics and tooth sensitivity. At least 14 different subtypes of amelogenesis imperfect exist with numerous patterns of inheritance and a variety of clinical manifestations. On the clinical and radiographic basis,three broad types exist,i.e. hypoplastic, hypocalcified and hypomaturation. This clinical report describes the management of a 12 year old girl with hypomaturation type of AI. The patient presented with mottled opaque white to yellow brown enamel affecting all teeth. Patient’s main concern was esthetic. The enamel was hard and the cusps on molars were intact.Initially preventive measures were advised to the patient followed by placement of stainless steel crowns on all the first permanent molars. This was followed by composite veneering on all the anterior teeth. The performed treatment achieved satisfactory esthetic and function, which resulted in an improvement in the child’s quality of life.