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Cat-Map Chromosome 8

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Cat-Map Chromosome 8 shiels.lab 11/6/2011









Cytogenet Physical Gene Exon/ DNA Change Coding Change Inh* Origin Cataract Phenotype Other Phenotype Reference Mouse Mouse Reference Rat Rat Reference

ic Locus Locus (Mbp) Intron Locus/Mutant Locus/Mutant

8p23.2- ? AR Pakistan Laminar, nuclear Sabir et al. 2010

p21.3

8p23.1- FDFT1 14 Fdft1 15 Fdft1

p22

? ? Shumiya cataract Mori et al. 2006

rat (SCR)

8p22 NAT2 Slow Cx S. Africa Age-related Meyer et al. 2003 8 Nat2

8p22 NAT2 NAT2*6A (slow) Cx Turkey Age-related Tamer et al. 2005

8p21.3 BIN3 14 Bin3

null Ramalingam et al. 2008

8p21.2 DOCK5 14 Dock5

rlc Omi et al. 2008

8p21.1 ESCO2 AR Roberts syndrome 14 Esco2

8p12- WRN AR Presenile posterior Werner syndrome http://www.pathology. 8 Wrn

p11.2 subcapsular washington.edu/resear

ch/werner/database/



8p12- WRN Ex35 c.4099T>C p.C1367R Cx Israel Age-related nuclear Ehrenberg et al. 2010

p11.2 rs1346044 (no association)



8p12-p11 IDO1 IVS4 rs4613984 (G>A) Cx India Age-related nuclear & Mamata et al. 2011 8 Ido1

posterior sub-capsular

8p11.22 ADAM9 AR Small posterior Cone-rod dystrophy-9 (CORD9) 8 Adam9

subcapsular

8q13.3 72,109,668… EYA1 Ex10 c.988G>A p.E330K AD Japan Persistence of pupilary membrane Azuma, et al. 2000 1 Eya1

72,274,467



8q13.3 EYA1 Ex12 c.1177G>A p.G393S AD Japan Nuclear-type, Brachio-oto-renal syndrome-1 Azuma, et al. 2000

congenital (BOR1), nystagmus

8q13.3 EYA1 Ex15 c.1320G>A p.R407Q AD Japan Nuclear-type, Central corneal opacity, Peters' Azuma, et al. 2000

congenital anomaly

8q21 NBN AR Nijmegen breakage syndrome 4 Nbn

null Yang et al. 2006

8q21.1 PXMP3 AR Zellweger syndrome-3 3 Pxmp3

8q21-q22 CNGB3 AR Achromatopsia-3 4 Cngb3

8q24.3 RECQL4 AR Subcapsular Rothmund Thompson syndrome 15 Recql4



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